SAFE Study: Safety of APCC Following Emicizumab Prophylaxis

Description

The purpose of the aPCC-emicizumab safety study is to investigate the hemostatic efficacy as measured by thrombin generation, of a low personalized dose of aPCC (FEIBA) in children and adults with hemophilia A and inhibitors on emicizumab prophylaxis.

Conditions

Hemophilia a

Study Overview

Study Details

Study overview

The purpose of the aPCC-emicizumab safety study is to investigate the hemostatic efficacy as measured by thrombin generation, of a low personalized dose of aPCC (FEIBA) in children and adults with hemophilia A and inhibitors on emicizumab prophylaxis.

APCC and Emicizumab Safety Study in Congenital Hemophilia a Patients with Inhibitors (SAFE Study: Safety of APCC Following Emicizumab Prophylaxis)

SAFE Study: Safety of APCC Following Emicizumab Prophylaxis

Condition
Hemophilia a
Intervention / Treatment

-

Contacts and Locations

Atlanta

Children's Healthcare of Atlanta, Atlanta, Georgia, United States, 30322

Atlanta

Emory University Hospital, Atlanta, Georgia, United States, 30322

Participation Criteria

Researchers look for people who fit a certain description, called eligibility criteria. Some examples of these criteria are a person's general health condition or prior treatments.

For general information about clinical research, read Learn About Studies.

Eligibility Criteria

  • * Moderately severe hemophilia A, defined as FVIII level \<0.05 IU/mL before development of an inhibitor
  • * Age ≥6 years of age at time of informed consent
  • * Documented on 2 occasions a high titer inhibitor (\>5 BU/mL) with a 72-hour washout within 2 years of enrollment
  • * Parent/guardian (Legally Authorized Representative) or the patient has provided written informed consent
  • * Adequate hematologic function (Hgb \>8 g/dL and platelet count \>100,000 µL)
  • * Adequate hepatic function (total bilirubin ≤1.5 x ULN and both AST/ALT ≤3x ULN at screening (excluding known Gilbert's)
  • * Adequate renal function (≤2.5 x ULN and CrCl ≥30 mL/min)
  • * Inherited or acquired bleeding disorder other than hemophilia A excluding low VWF (\>30% VWF:RCo or VWF:GP1bm)
  • * Had an active bleed requiring factor therapy at screening
  • * Previous or current treatment for thromboembolic disease or signs of thromboembolic disease (excluding previously resolved line-associated thrombosis)
  • * Had a surgical procedure 14 days before screening
  • * Conditions that may increase the risk of bleeding or thrombosis
  • * If the patient is treated with rFVIIa or aPCC seven days before screening
  • * History of clinically significant hypersensitivity associated with monoclonal antibody therapies or components of the emicizumab injection
  • * Had current use of any medication other than emicizumab that could affect the coagulation system.
  • * Known HIV infection with CD4 count \<200 cells/µL within 24 weeks before screening. Testing is not required if \<35 years of age.
  • * Use of systemic immunomodulators at enrollment or planned use during the study
  • * Participants who are at high risk for TMA (for example, have a previous medical/family history of TMA), in the investigator's judgment
  • * Concurrent disease, treatment, or abnormality in clinical laboratory tests that could interfere with the conduct of the study, may pose an additional risk, or would, in the opinion of the investigator, preclude the participant's safe participation in and completion of the study

Ages Eligible for Study

6 Years to

Sexes Eligible for Study

ALL

Accepts Healthy Volunteers

No

Collaborators and Investigators

Emory University,

Robert Sidonio, MD, PRINCIPAL_INVESTIGATOR, Emory University

Study Record Dates

2025-09