129 Xenon MRI As a Biomarker for Diagnosis and Response to Therapy in Pulmonary Arterial Hypertension (PAH)

Description

The overall study objectives outlined in this study are to derive 129Xe MRI pulmonary vascular biomarker signatures that differentiate common subtypes of PAH and to determine the ability of 129Xe MRI to longitudinally monitor disease progression and response to therapy in PAH, with the aid of additional assessments, such as labs, echocardiography, and six-minute walk distance (6MWD).

Conditions

Pulmonary Arterial Hypertension, Idiopathic Pulmonary Arterial Hypertension, Pulmonary Arterial Hypertension Associated with Connective Tissue Disease (Disorder), Connective Tissue Diseases

Study Overview

Study Details

Study overview

The overall study objectives outlined in this study are to derive 129Xe MRI pulmonary vascular biomarker signatures that differentiate common subtypes of PAH and to determine the ability of 129Xe MRI to longitudinally monitor disease progression and response to therapy in PAH, with the aid of additional assessments, such as labs, echocardiography, and six-minute walk distance (6MWD).

129 Xenon MRI As a Biomarker for Diagnosis and Response to Therapy in Pulmonary Arterial Hypertension (PAH)

129 Xenon MRI As a Biomarker for Diagnosis and Response to Therapy in Pulmonary Arterial Hypertension (PAH)

Condition
Pulmonary Arterial Hypertension
Intervention / Treatment

-

Contacts and Locations

Durham

Duke University Medical Center, Durham, North Carolina, United States, 27710

Participation Criteria

Researchers look for people who fit a certain description, called eligibility criteria. Some examples of these criteria are a person's general health condition or prior treatments.

For general information about clinical research, read Learn About Studies.

Eligibility Criteria

  • * Age: 18-75 years
  • * WHO functional class 2 or 3
  • * Mean pulmonary artery pressures \> 20 mmHg
  • * Pulmonary capillary wedge pressure ≤15 mmHg
  • * Pulmonary vascular resistance \> 2 Wood Units (WU)
  • * No other cause identified for PAH
  • * Age: 18-75 years
  • * WHO functional class (FC) 2 or 3
  • * Mean pulmonary artery pressures \> 20 mmHg
  • * Pulmonary capillary wedge pressure ≤15 mmHg
  • * Pulmonary vascular resistance \> 2 WU
  • * Diagnosis of connective tissue disease
  • * PH other than Idiopathic PAH or PAH associated with CTD; any conditions that prevent the performance of 129Xe MRI scans will be excluded from the study.

Ages Eligible for Study

18 Years to 75 Years

Sexes Eligible for Study

ALL

Accepts Healthy Volunteers

No

Collaborators and Investigators

Bastiaan Driehuys,

Fawaz Alenezi, MD, PRINCIPAL_INVESTIGATOR, Duke Univeristy

Study Record Dates

2026-03-31